Spindle Cell Sarcoma of Pharynx: A Rare Case with Successful Management

Abstract

Introduction

Spindle cell sarcoma is a rare and aggressive malignancy characterized by spindle-shaped tumour cells. It can arise from various anatomical sites from soft tissue or bone. Involvement of the pharynx is relatively rare. This case report presents a unique case of spindle cell sarcoma in the pharynx, initially  misdiagnosed as a vallecular space-occupying lesion on Fiber Optic Laryngoscopy but later confirmed as arising from the lateral wall of pharynx on HRCT. Accurate diagnosis and prompt management are essential for optimizing patient outcomes.

Case Report

A 57-year-old male patient presented to the ENT clinic with a two-month history of stridor and difficulty in swallowing. The patient had no significant medical or surgical history. Fibre optic laryngoscopy revealed a large vallecular space-occupying lesion obstructing the airway and impeding deglutition. The patient was scheduled for surgery after a thorough clinical and radiological evaluation. Contrast enhanced CT scan reveals SOL arising from the left side of pharynx with contrast uptake.

Discussion

Spindle cell sarcoma of the pharynx is a rare entity with limited reported cases. It poses a diagnostic challenge due to its atypical presentation and overlapping histopathological features with other spindle cell tumours. Immuno histochemistry plays a crucial role in confirming the diagnosis by evaluating specific markers. Surgical excision remains the primary treatment modality, often combined with adjuvant therapy depending on the stage and extent of the disease.